Which of the following conditions is associated with marfanoid habitus?

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Marfanoid habitus refers to a body type characterized by tall stature, long limbs, arachnodactyly (long fingers), and other connective tissue features. Beals syndrome is the condition that is most closely associated with marfanoid habitus. It is a genetic disorder that shares similarities with Marfan syndrome, particularly in its musculoskeletal manifestations. Individuals with Beals syndrome often display the characteristic tall, slender build and long fingers that define marfanoid habitus.

The condition is caused by mutations in the FBN2 gene, which is involved in the formation of connective tissue. The presence of this marfanoid body structure, coupled with other features such as joint contractures and scoliosis, allows healthcare professionals to identify Beals syndrome as being inherently linked to marfanoid habitus.

While other conditions listed can have overlapping features, they do not typically present with the pronounced marfanoid characteristics seen in Beals syndrome. Carney syndrome, Stickler syndrome, and Noonan syndrome each have their unique clinical features and may include some skeletal or connective tissue manifestations, but they do not define or strongly associate with marfanoid habitus as Beals syndrome does.

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